Skip to main content

CPS 1 Activator

Carbamoyl Phosphate Synthetase 1 (CPS 1) activators are used to treat excess levels of ammonia in the blood (hyperammonemia). They act as a replacement for an enzyme that converts ammonia into urea so it can be safely eliminated from the body.

Why are cps 1 activator prescribed?

  1. Hyperammonemia (100%)

Key takeaways

Carbamoyl phosphate synthetase 1 (CPS 1) is used to treat hyperammonemia caused by N-acetylglutamate synthase (NAGS) deficiency. It works by enhancing the activity of CPS-1, an enzyme that helps remove excess ammonia from your body. An example of a CPS-1 activator is carglumic acid (Carbaglu).

Prices for popular CPS 1 Activator medications
Viewing 1 of 1 medications
tablet icon

Carbaglu (carglumic acid)

as low as$1,846
CARGLUMIC ACID treats urea cycle disorders (UCDs). It works by helping your body decrease the amount of ammonia in your blood. This lowers the risk of serious health problems. It is not a cure.
See pricesMore info
Disclaimer: Popularity is based on total prescriptions for the brand and generic versions of each drug, regardless of the condition being treated. Some drugs are prescribed for multiple conditions.

Subscribe and save

Get prescription saving tips and more from GoodRx Health. Enter your email to sign up

By signing up, I agree to GoodRx’s Terms of Use and Privacy Policy, and to receive marketing messages from GoodRx.

Browse medications

View All
Research prescriptions and over-the-counter medications from A to Z, compare drug prices, and start saving.
ABCDEFGHIJKLMNOPQRSTUVWXYZ