What Is Idiopathic Pulmonary Fibrosis?

Idiopathic Pulmonary Fibrosis (IPF) is a chronic condition where the lungs become scarred and stiffen, and breathing becomes more difficult. Idiopathic means the cause is unknown, and pulmonary fibrosis refers to the scarring of the lung tissue. Symptoms can include shortness of breath, cough, and chest pain.

There is no known cure for IPF, though some medications may help relieve symptoms or prolong life. However, most people with IPF get worse over time, even with treatment. Newly approved drugs like Ofev and Esbriet may help delay progression. Non-medication therapies like oxygen and lung transplants can also improve quality and length of life.